Table 1. Clinical characteristics of pheochromocytoma patients

Age at diagnosis/Gender Adrenal tumor (size on CT imaging) Syndromic manifestations 24h-Urinary catecholamine (μg/24h) Plasma metanep hrine (<90pg/mL) Calciton in (<6.4pg/ mL) CEA (<5ng/mL) Calciu m (mmol /L) iPTH (21-45pg/ mL) Genetic mutation
Adren alin (<20) Noradre nalin (<90) Dopa mine (<600)
BN 01 30/F Unilateral L: 30x40x50 mm No 57.9 340.7 430.5 64.5 5.1 3.2 2.48 33.9 ND
BN 02 32/M Bilateral L: 20x30x35 mm R: 40x45x40 mm No 13.1 250.4 500.4 102.5 4.2 2.2 2.52 20.1 ND
BN 03 33/F Bilateral L: 40x50x60 mm R: 50x40x55 mm No 7.6 199 278.3 758 4.1 3.8 2.30 29.8 RET gene: c.1900T >C (Cys634 Arg)
BN 04 34/M Bilateral L: 15x20x20 mm R: 25x40x30 mm No 133.3 116.4 568.4 589.8 57.2 14.6 2.42 25.4 RET gene: c.1900T >G (Cys634 Gly)
BN 05 41/M Bilateral L: 12x10x10 mm* R: 60x90x70 mm MEN2A (MTC & PC) 460.0 1098.6 1228.4 1102.0 869.0 85.5 2.34 33.6 RET gene: c.1900T >C (Cys634 Arg)
BN 06 25/F Bilateral L: 59x55x40 mm R: 36x48x25 mm* MEN2A (MTC & PC) 76.2 210 462.0 861.3 28.6 33.5 2.20 42.5 RET gene: c. >C (Cys634 Arg)
BN 07 30/F Bilateral L: 15x20x20 mm R: 25x40x30 mm MEN2A (MTC & Bilateral PC) 800 311 1400.0 717.0 2069 51.8 2.32 46 RET gene: c.1900T >C (Cys634 Arg)
M, Male; F, Female
L, left pheochromocytoma tumor; R, right pheochromocytoma tumor ND, not detectable
PC, Pheochromocytoma
MTC, Medullary thyroid carcinoma
First PC diagnosis followed by subsequent PC diagnosis in contralateral gland.